Hailey-Hailey Disease - Symptoms, Causes, Treatment | NORD
WEBOct 25, 2023 · Hailey-Hailey disease is a rare genetic disorder that is characterized by blisters and erosions most often affecting the neck, armpits, skin folds and genitals. The lesions may come and go and usually heal without scarring. Sunlight, heat, sweating and friction often aggravate the disorder.
Hailey-Hailey disease (benign familial pemphigus) - DermNet
WEBAug 2, 2017 · It is a rare hereditary blistering skin disease first described by the Hailey brothers in 1939. Unrelated to pemphigus vulgaris, Hailey-Hailey disease is not an autoimmune condition and has a differing prognosis.
Hailey-Hailey disease (benign familial pemphigus) - UpToDate
WEBMar 4, 2024 · Hailey-Hailey disease (HHD; MIM #169600), also called benign familial pemphigus or benign chronic pemphigus, is a rare, autosomal dominant disorder that affects the adhesion of epidermal keratinocytes.
Benign Familial Pemphigus (Hailey-Hailey Disease) - StatPearls
WEBAug 14, 2023 · The typical skin lesions of Hailey-Hailey disease usually occur in friction or intertriginous areas, including the sides and back of the neck, axillary, inguinal, and perineal folds (scrotum, vulva). The sub-mammary area affects as much as 50% of female patients with HHD.
Hailey-Hailey disease - MedlinePlus
WEBHailey-Hailey disease, also known as benign chronic pemphigus, is a rare skin condition that usually appears in early adulthood. The disorder is characterized by red, raw, and blistered areas of skin that occur most often in skin folds, such as the groin, armpits, neck, and under the breasts.
Hailey–Hailey disease - Wikipedia
WEBHHD is characterized by outbreaks of rashes and blisters on the skin. Affected areas of skin undergo repeated blistering and inflammation, and may be painful to the touch. Areas where the skin folds, as well as the armpits, groin, neck, buttocks and under the breasts are most commonly affected.
About HHD | Hailey-Hailey Disease Society
WEBHHD, Hailey-Hailey Disease or Chronic Benign Familial Pemphigus, is a genetic acantholytic (blistering) skin condition resulting from a mutation on one copy of chromosome 3 that encodes the protein ATP2C1. The mutation is found specifically at location 3.q22.1.
Hailey-Hailey Disease (Benign Familial Chronic Pemphigus, Benign ...
WEBMar 13, 2019 · Patients with extensive skin involvement with Hailey-Hailey disease may develop a flare with associated vesicles and bullae. Clinicians should consider the possibility of eczema herpeticum in such cases and confirm the diagnosis with a Tzanck preparation, skin biopsy, or culture, and institute prompt antiviral therapy.
Hailey-hailey disease - British Skin Foundation
WEBIt is a rare inherited skin condition in which there are red scaly areas that can be itchy and sore, that can lead to superficial blisters and eroded (broken) areas of the skin. This usually affects the folds of the groin, armpits, neck and under the breasts.
Familial Benign Pemphigus (Hailey-Hailey Disease) - Medscape
WEBFamilial benign pemphigus is a chronic autosomal dominant disorder with incomplete penetrance. Approximately two thirds of patients with familial benign pemphigus have a family history of...
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